Aka monosuperocentroincisivodontic dwarfism.

Presentation

Midline symmetrical upper central incisor.
The condition may also be associated with other midline disturbances such as

  • cleft palate
  • choanal stenosis or atresia
  • imperforate anus, or
  • umbilical hernia.
  • It is part of the spectrum of the holoprosencephaly malformation complex.
    Of importance is the association with hypoplasia of the sella, pituitary dysfunction, growth hormone deficiency and subsequent short stature.


    Adapted from "Handbook of Pediatric Dentistry" Editors: Cameron, Widmar. Mosby - Wolfe.

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